Remission of Congenital Multi-system Type Langerhans Cell Histiocytosis with Chemotherapy
2019
Patients with multi-system (MS)-type
langerhans cell histiocytosis(LCH) show poor outcomes, especially congenital MS LCH cases were shown in high mortality rate. We experienced a congenital case of MS LCH with high risk organs, who needed intensive respiratory support after birth. Even though intensive
chemotherapywas discontinued, this patient’s lung LCH lesions gradually became reduced and his respiratory condition recovered; therefore, we restarted and completed maintenance
chemotherapy. The patient maintained complete remission for more than 4 years after the end of
chemotherapy. Our case suggests that congenital MS LCH even with severe organ involvement can be treated successfully with
chemotherapy.
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