Abstract 13841: Aortic and Pulmonary Dissections in Women With Turner Syndrome

Introduction: While aortic dissection in women with Turner syndrome (TS) has been well reported, other vascular dissections, including pulmonary artery (PA) dissections, have not been noted. In 2007, national guidelines were published to improve the care of women with TS and included recommendations for routine echocardiographic screening. Hypothesis: We sought to determine the incidence of vascular dissections in women with TS cared for since publication of the new guidelines and to assess for clinical correlates of such. Methods: Multi-centered retrospective data review of all cardiac, echocardiographic, endocrine, medicine and inpatient records was performed in patients with TS seen for clinical evaluation by any provider since 2007 at 3 institutions. Results: Of 603 patients identified, 395 were > 18 years of age at last visit. Within this cohort of adults, 75 (19%) were never referred to a cardiologist during their lifetime. At least 1 echocardiogram was performed in all but 27 (7%) patients. Since 2...