Combination of Left Ventricular Noncompaction and Bicuspid Aortic Valve in 19-Year-Old Male: A Case Report from Republic of Macedonia

Background: Noncompaction of the ventricular myocardium is a rare, unclassified cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings consist of multiple, prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. Aim: The aim of this report was to present the first case of noncompaction cardiomyopathy with bicuspid aortic valve in Republic of Macedonia. Case Report: A 19-year-old male with the diagnosis of syncope, tachycardia with arrhythmia, and chest pain was referred to the University Clinic of Cardiology for the echocardiography. Transthoracic echocardiography showed bicuspid aortic valve with normal left ventricular (LV) dimensions and normal systolic function. Mild thickening of the aortic valve cusps and mild aortic regurgitation was found. In addition to these echocardiographic findings, prominent muscular trabeculations and deep intertrabecular spaces communicating with the ventricular cavity were observed in the infero-postero-lateral region, apical and septal portion of the LV chamber. Conclusion: We described first case of combination of left ventricular noncompaction and bicuspid aortic valve in 19-year-old male in the Republic of Macedonia.