Cardiomyopathie hypertrophique familiale associée à un syndrome de Wolff-Parkinson-White

AbstractFamilial hypertrophic cardiomyopathy (HCM) with Wolff-Parkinson-White (WPW) syndrome is extremely rare and associated with a high risk of ventricular tachyarrhythmia and sudden death. We report a familial form of hypertophic cardiomyopathy associated with Wolff-Parkinson-White syndrome in two siblings 7 and 12-year-old. These patients showed progression to left ventricular dilatation.Early recognition and treatment of such forms can improve such evolution and the risk of sudden death.