At Ross-Konno Operation in an Infant with a Quadricuspid Pulmonary Valve and Anomalous Aortic Origin of the Right Coronary Artery

Abstract Anomalous aortic origin of the right coronary artery (AAORCA) from the left aortic sinus is a rare congenital anomaly, which is generally repaired during adolescence when associated with symptoms. It is rarely diagnosed in infancy. Similarly, a Quadricuspid Pulmonary valve (QPV) is also a rare finding and there is scant data to evaluate whether this malformation of the pulmonary valve is suitable to be used for a Ross operation [1-3]. We describe a unique case in which both these anomalies co-existed in an infant who underwent a successful Ross-Konno operation.