Lingual thyroid with coexisting normal thyroid (one lobe) in neck

Ectopic thyroid tissue not located anterolaterally to the second and fourth tracheal cartilage is rare. In majority of the cases, it is located in the midline between foramen cecum and the usual location of thyroid gland in the neck. Most often, it is found in the base of the tongue. We present a case of lingual thyroid with hemi-agenesis of right lobe and colloid nodule in left lobe presenting with difficulty in breathing and swallowing with choking episodes since the last 9 months. The patient was operated upon under general anesthesia, and the lingual mass was removed intraorally leaving a minimal part and sent for histopathological examination, which ultimately confirmed the diagnosis of lingual thyroid tissue. We are presenting this case for its rarity in general practice and because of its unusual presentation.