Primary Ewing's sarcoma of the sphenoid sinus with orbital and intracranial extension: a case report.

Ewing's sarcomais a high-grade neuroectodermal primary bonetumor. This is the second primary bonetumor in children afterosteosarcoma and represents 4 to10% of cases. It can occur in all skeletal bones. However, the location at the facial bonesis uncommon (1to2%) and extremely rare at the sphenoid sinus. We report the clinical results of a rare case of Ewing's sarcomaof the sphenoid with intraorbitaland intracranial extension.