Pulmonary arterial hypertension in idiopathic inflammatory myopathies: Data from the French pulmonary hypertension registry and review of the literature

AbstractOccurrence of pulmonary arterial hypertension (PAH) in idiopathic inflammatory myopathies(IIMs) without extensive interstitial lung disease(ILD) has rarely been described in the medical literature. This study aimed to report all caseswith association of PAH and IIM in the French Pulmonary